Tacrolimus and Methotrexate With or Without Sirolimus in Preventing Graft-Versus-Host Disease in Young Patients Undergoing Donor Stem Cell Transplant for Acute Lymphoblastic Leukemia in Complete Remission

This study has been completed.
Sponsor:
Collaborator:
Information provided by (Responsible Party):
Children's Oncology Group
ClinicalTrials.gov Identifier:
NCT00382109
First received: September 26, 2006
Last updated: June 14, 2013
Last verified: June 2013
  Purpose

This randomized phase III trial is studying tacrolimus, methotrexate, and sirolimus to see how well they work compared to tacrolimus and methotrexate in preventing graft-versus-host disease in young patients who are undergoing donor stem cell transplant for intermediate-risk or high-risk acute lymphoblastic leukemia in second complete remission. Giving chemotherapy, such as thiotepa and cyclophosphamide, and total-body irradiation before a donor stem cell transplant helps stop the growth of cancer cells. It also helps stop the patient's immune system from rejecting the donor's stem cells. The donated stem cells may replace the patient's immune cells and help destroy any remaining cancer cells (graft-versus-tumor effect). Sometimes the transplanted cells from a donor can also make an immune response against the body's normal cells. Giving tacrolimus, methotrexate, and sirolimus after the transplant may stop this from happening. It is not yet known whether tacrolimus and methotrexate are more effective with or without sirolimus in preventing graft-versus-host disease.


Condition Intervention Phase
B-cell Childhood Acute Lymphoblastic Leukemia
Childhood Acute Lymphoblastic Leukemia in Remission
Graft Versus Host Disease
L1 Childhood Acute Lymphoblastic Leukemia
L2 Childhood Acute Lymphoblastic Leukemia
T-cell Childhood Acute Lymphoblastic Leukemia
Drug: thiotepa
Drug: cyclophosphamide
Drug: tacrolimus
Drug: methotrexate
Drug: sirolimus
Radiation: total body irradiation
Phase 3

Study Type: Interventional
Study Design: Allocation: Randomized
Endpoint Classification: Safety/Efficacy Study
Intervention Model: Parallel Assignment
Masking: Open Label
Primary Purpose: Treatment
Official Title: A Randomized Trial of Sirolimus-Based Graft Versus Host Disease Prophylaxis After Hematopoietic Stem Cell Transplantation in Relapsed Acute Lymphoblastic Leukemia

Resource links provided by NLM:


Further study details as provided by Children's Oncology Group:

Primary Outcome Measures:
  • Event-free survival after transplantation as measured by the O'Brien-Fleming spending function [ Time Frame: Up to 2 years ] [ Designated as safety issue: No ]

Secondary Outcome Measures:
  • Rate of relapse [ Time Frame: Up to 1 year ] [ Designated as safety issue: No ]
  • Rate of treatment-related mortality [ Time Frame: Up to 100 days ] [ Designated as safety issue: Yes ]
    A one-sided Z-test of proportions (alpha = 0.05) will be used

  • Rate of acute graft-versus-host-disease (GVHD) [ Time Frame: Up to 3 months ] [ Designated as safety issue: Yes ]
    A two-sided Z-test of proportions (alpha = 0.05) will be used.

  • Rate of chronic GVHD [ Time Frame: Up to 5 years ] [ Designated as safety issue: Yes ]
    A two-sided log-rank test (alpha = 0.05) will be used.

  • Relative contribution of resistance by acute lymphoblastic leukemia (ALL) blasts to cytolytic therapy (e.g., chemotherapy/irradiation) as a cause of relapse post-transplantation [ Time Frame: Up to 1 year ] [ Designated as safety issue: No ]
    Contingency tables will be used to tabulate relapse with first complete remission (CR1) ALL blast sirolimus resistance and sirolimus biomarkers. Second complete remission (CR2) ALL blast sirolimus resistance and biomarkers will be compared to CR1 ALL blast levels with McNemar‟s test.

  • Relative contribution of resistance by ALL blasts to the donor immune response as a cause of relapse post-transplantation [ Time Frame: Up to 1 year ] [ Designated as safety issue: No ]
    Multivariate analyses of relapse risk and treatment resistance will be performed using logistic regression.

  • MRD [ Time Frame: Up to 9 months ] [ Designated as safety issue: No ]
    A mixed effects model will be fit with the covariates used.

  • Chimerism [ Time Frame: Up to 12 months ] [ Designated as safety issue: No ]
    A mixed effects model will be fit with the covariates used.


Enrollment: 146
Study Start Date: March 2007
Primary Completion Date: October 2012 (Final data collection date for primary outcome measure)
Arms Assigned Interventions
Experimental: Arm I (experimental)
Patients will receive the designated preparative regimen of cyclophosphamide/total body irradiation (TBI)/Thiotepa starting at day -8. Patients receive tacrolimus IV continuously or orally (when able) daily beginning on day -2 followed by a taper beginning on day 42 and continuing until day 98 (for patients undergoing matched sibling donor transplantation) OR tacrolimus IV continuously or orally daily beginning on day -2 followed by a taper beginning on day 100 and continuing until day 180 (for patients undergoing related, unrelated, or cord blood donor transplantation) in the absence of GVHD. Patients also receive methotrexate IV on days 1, 3, and 6 (for patients with matched sibling and umbilical cord blood donors) OR days 1, 3, 6, and 11 (for patients with unrelated bone marrow and peripheral blood stem cell donors) and oral sirolimus daily beginning on day 0 followed by a taper beginning on day 180 and continuing until day 207.
Drug: thiotepa
Given IV
Other Names:
  • Oncotiotepa
  • STEPA
  • TESPA
  • Tespamin
  • TSPA
Drug: cyclophosphamide
Given IV
Other Names:
  • CPM
  • CTX
  • Cytoxan
  • Endoxan
  • Endoxana
Drug: tacrolimus
Given IV or orally
Other Names:
  • FK 506
  • Prograf
Drug: methotrexate
Given IV
Other Names:
  • amethopterin
  • Folex
  • methylaminopterin
  • Mexate
  • MTX
Drug: sirolimus
Given orally
Other Names:
  • AY 22989
  • Rapamune
  • rapamycin
  • SLM
Radiation: total body irradiation
Part of the transplant preparatory regimen
Other Name: TBI
Active Comparator: Arm II (control)
Patients receive tacrolimus and methotrexate as in arm I.
Drug: thiotepa
Given IV
Other Names:
  • Oncotiotepa
  • STEPA
  • TESPA
  • Tespamin
  • TSPA
Drug: cyclophosphamide
Given IV
Other Names:
  • CPM
  • CTX
  • Cytoxan
  • Endoxan
  • Endoxana
Drug: tacrolimus
Given IV or orally
Other Names:
  • FK 506
  • Prograf
Drug: methotrexate
Given IV
Other Names:
  • amethopterin
  • Folex
  • methylaminopterin
  • Mexate
  • MTX
Radiation: total body irradiation
Part of the transplant preparatory regimen
Other Name: TBI

Detailed Description:

PRIMARY OBJECTIVES:

I. Compare the post-transplant 2-year event-free survival of pediatric patients with intermediate-risk or high-risk acute lymphoblastic leukemia (ALL) in second complete remission undergoing allogeneic hematopoietic stem cell transplantation treated with graft-versus-host disease (GVHD) prophylaxis comprising tacrolimus and methotrexate with or without sirolimus.

SECONDARY OBJECTIVES:

I. Compare rates of relapses, transplant-related mortality, and acute and chronic GVHD in these patients.

II. Evaluate the relative contribution of resistance by ALL blasts to cytolytic therapy (e.g., chemotherapy/irradiation) as a cause of relapse post-transplantation by correlating ALL in vivo blast resistance with in vivo sirolimus, inhibition levels of the mTOR pathway in patients treated with sirolimus, and altered resistance pathways in ALL blasts measured by microarray analysis.

III. Evaluate the relative contribution of resistance by ALL blasts to the donor immune response as a cause of relapse post-transplantation by correlating the development of donor anti-ALL T-cell response, the development of acute and/or chronic GVHD, and the detection of altered ALL blast immunogenicity after transplant with increased minimal residual disease, persistent recipient chimerism, and relapse.

OUTLINE: This is a randomized, open-label, multicenter study. Patients are stratified according to risk (intermediate CR2 vs high CR2 vs very high CR1), donor type (matched sibling vs unrelated or mismatched vs mismatched related), and stem cell source (filgrastim [G-CSF]-primed bone marrow vs unprimed bone marrow vs bone marrow vs peripheral blood vs umbilical cord blood).

PREPARATIVE REGIMEN: Patients undergo total-body irradiation twice daily on days -8 to -6 and receive thiotepa IV on days -5 and -4 and cyclophosphamide IV on days -3 and -2.

ALLOGENEIC HEMATOPOIETIC STEM CELL TRANSPLANTATION: Patients undergo allogeneic hematopoietic stem cell transplantation on day 0.

GRAFT-VERSUS-HOST DISEASE (GVHD) PROPHYLAXIS: Patients are randomized to 1 of 2 treatment arms.

ARM I: (experimental) Patients receive tacrolimus IV continuously or orally (when able) daily beginning on day -2 followed by a taper beginning on day 42 and continuing until day 98 (for patients undergoing matched sibling donor transplantation) OR tacrolimus IV continuously or orally daily beginning on day -2 followed by a taper beginning on day 100 and continuing until day 180 (for patients undergoing related, unrelated, or cord blood donor transplantation) in the absence of GVHD. Patients also receive methotrexate IV on days 1, 3, and 6 (for patients with matched sibling and umbilical cord blood donors) OR days 1, 3, 6, and 11 (for patients with unrelated bone marrow and peripheral blood stem cell donors) and oral sirolimus daily beginning on day 0 followed by a taper beginning on day 180 and continuing until day 207.

ARM II: (control) Patients receive tacrolimus and methotrexate as in arm I.

After completion of study treatment, patients are followed periodically for approximately 10 years.

  Eligibility

Ages Eligible for Study:   1 Year to 21 Years
Genders Eligible for Study:   Both
Accepts Healthy Volunteers:   No
Criteria

Inclusion Criteria:

  • Histologically or cytologically confirmed acute lymphoblastic leukemia (ALL)* in second complete remission (CR2) (M1 bone marrow, < 5% blasts by morphology) meeting the following criteria:

    • Eligible for matched sibling transplantation AND intermediate-risk disease meeting 1 of the following criteria:

      • B-lineage ALL in CR2 after a late first bone marrow (BM) relapse (≥ 36 months after the initiation of primary chemotherapy) with or without associated extramedullary disease
      • B-lineage ALL in CR2 after a very early isolated extramedullary relapse**
    • Eligible for other related donor, unrelated donor, or matched sibling transplantation AND high-risk disease meeting 1 of the following criteria:

      • In CR2 after an early first BM relapse (< 36 months from initiation of primary chemotherapy)
      • T-lineage ALL in CR2 after a first BM relapse occurring at any time after initiation of primary chemotherapy
      • Philadelphia chromosome-positive ALL in CR2 after a first BM relapse occurring at any time after the initiation of primary chemotherapy
      • T-lineage ALL in CR2 after a very early isolated extramedullary relapse**
  • Enrolled on an appropriate COG relapsed ALL clinical trial meeting 1 of the following criteria:

    • Must proceed directly to transplantation after completing the required study therapy (i.e., 1 induction course and 2 consolidation courses)
    • Patients not on a COG relapsed ALL clinical trial are eligible provided they have received ≥ 1 round of re-induction lasting 4-6 weeks and 1 round of intensive consolidation chemotherapy lasting 3-6 weeks
  • No B-cell ALL L3 morphology with evidence of myc translocation by molecular or cytogenetic technique
  • No Down syndrome
  • No evidence of active CNS or other extramedullary disease (i.e., no CNS2)
  • Karnofsky performance status (PS) 60-100% (for patients > 16 years of age) OR Lansky PS 60-100% (for patients ≤ 16 years of age)
  • Shortening fraction ≥ 27% by echocardiogram OR ejection fraction ≥ 50% by radionuclide angiogram
  • ALT or AST < 5 times upper limit of normal
  • Bilirubin < 2.5 mg/dL (unless an increase is attributable to Gilbert's syndrome)
  • Creatinine clearance OR radioisotope glomerular filtration rate ≥ 70 mL/min
  • FEV_1 ≥ 60% by pulmonary function tests (PFTs)
  • FVC ≥ 60% by PFTs
  • DLCO ≥ 60% by PFTs
  • For children who are unable to cooperate for PFTs all of the following criteria must be met:

    • No evidence of dyspnea at rest
    • No exercise intolerance
    • No requirement for supplemental oxygen therapy
  • Not pregnant or nursing
  • Negative pregnancy test
  • Fertile patients must use effective contraception
  • No HIV or uncontrolled fungal, bacterial, or viral infection

    • Fungal infection acquired during induction therapy allowed provided there is a significant response to antifungal therapy with minimal or no evidence of disease by CT scan
  • Other concurrent immunosuppressants allowed
  • No prior allogeneic or autologous stem cell transplantation
  • No prior or concurrent voriconazole unless prior voriconazole therapy is completed or a different agent is substituted for voriconazole prior to study entry
  • No concurrent grapefruit juice during sirolimus administration
  Contacts and Locations
Please refer to this study by its ClinicalTrials.gov identifier: NCT00382109

  Show 50 Study Locations
Sponsors and Collaborators
Children's Oncology Group
Investigators
Principal Investigator: Michael Pulsipher Children's Oncology Group
  More Information

No publications provided

Responsible Party: Children's Oncology Group
ClinicalTrials.gov Identifier: NCT00382109     History of Changes
Other Study ID Numbers: ASCT0431, NCI-2009-01068, CDR0000500131, COG-PBMTC-ONCO51, COG-ASCT0431, U10CA098543
Study First Received: September 26, 2006
Last Updated: June 14, 2013
Health Authority: United States: Institutional Review Board

Additional relevant MeSH terms:
Graft vs Host Disease
Leukemia
Leukemia, Lymphoid
Precursor Cell Lymphoblastic Leukemia-Lymphoma
Immune System Diseases
Neoplasms by Histologic Type
Neoplasms
Lymphoproliferative Disorders
Lymphatic Diseases
Immunoproliferative Disorders
Cyclophosphamide
Methotrexate
Thiotepa
Sirolimus
Everolimus
Tacrolimus
Immunosuppressive Agents
Immunologic Factors
Physiological Effects of Drugs
Pharmacologic Actions
Antirheumatic Agents
Therapeutic Uses
Antineoplastic Agents, Alkylating
Alkylating Agents
Molecular Mechanisms of Pharmacological Action
Antineoplastic Agents
Myeloablative Agonists
Abortifacient Agents, Nonsteroidal
Abortifacient Agents
Reproductive Control Agents

ClinicalTrials.gov processed this record on June 18, 2013