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Found 11 studies with search of: ((primary immunodeficiency disease OR PIDD) AND NIAID) NOT (HIV OR AIDS) | Open Studies
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Rank Status Study
1 Recruiting Studies of Disorders in Antibody Production and Related Primary Immunodeficiency States
Conditions: Hyper-IgM Syndrome;   Ectodermal Dysplasia
Intervention:
2 Recruiting Establishing Fibroblast-Derived Cell Lines From Skin Biopsies of Patients With Immunodeficiency or Immunodysregulation Disorders
Conditions: Lymphohistiocytosis, Hemophagocytic;   Common Variable Immunodeficiency;   Severe Combined Immunodeficiency
Intervention:
3 Recruiting Genetic Analysis of Immune Disorders
Conditions: Healthy;   Immunologic Deficiency Syndrome;   Job's Syndrome;   Severe Combined Immunodeficiency
Intervention:
4 Recruiting Treatment for Growth Failure in Patients With X-Linked Severe Combined Immunodeficiency: Phase 2 Study of Insulin-Like Growth Factor-1
Conditions: Growth Failure;   X-linked Severe Combined Immunodeficiency (XSCID);   Growth Hormone Resistence
Interventions: Drug: Increlex;   Procedure: Arginine Provocation Test;   Procedure: Clonidine Provocation Test;   Procedure: IGF-1 Generation Test;   Drug: IVIG;   Procedure: Haplo-Identical Bone Marrow Transplant
5 Recruiting Antibody Production in Immune Disorders
Condition: Immunologic Disease
Intervention:
6 Recruiting Immune Regulation in Patients With Common Variable Immunodeficiency and Related Syndromes
Conditions: Agammaglobulinemia;   Common Variable Immunodeficiency;   Immunologic Deficiency Syndrome
Intervention:
7 Recruiting Natural History of Bronchiectasis
Conditions: Bronchiectasis;   Cystic Fibrosis;   Autoimmune Disease;   Common Variable Immunodeficiency
Intervention:
8 Recruiting Thymus Transplantation in DiGeorge Syndrome
Condition: DiGeorge Syndrome
Intervention: Other: Thymus Transplantation
9 Recruiting Host Factors in Invasive and Recurrent Staphylococcus Aureus Infection
Conditions: Staphylococcal Aureus Infection;   Recurrent Staphylococcal Infection;   Invasive Staphylococcal Infection
Intervention:
10 Recruiting Serum-Free Thymus Transplantation in DiGeorge Anomaly
Condition: DiGeorge Anomaly
Interventions: Other: Serum Free Thymus Transplantation with Immunosuppression;   Other: Serum Free Thymus Transplantation without immunosuppression
11 Recruiting Detection and Characterization of Infections and Infection Susceptibility
Conditions: Immune Disorders;   Chronic Granulomatous Disease;   Genetic Immunological Deficiencies;   Hyperimmunoglobulin-E Recurrent Infection Syndrome;   Recurrent Infections
Intervention:

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